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학술연구/단체지원/교육 등 연구자 활동을 지속하도록 DBpia가 지원하고 있어요.
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논문 기본 정보
- 자료유형
- 학술저널
- 저자정보
- 발행연도
- 2020.1
- 수록면
- 138 - 142 (5page)
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초록· 키워드
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Atypical hemolytic uremic syndrome (aHUS) is an extremely rare and life-threatening disorder. Typical HUS is often caused by Shiga toxin-positive Escherichia coli , while aHUS is caused by dysregulation of the alternative pathway of the complement system in association with genetic abnormalities or development of autoantibodies. Eculizumab, a humanized anti-complement 5 monoclonal antibody, is recommended for the treatment of aHUS, but its long-term safety and efficacy in pediatric patients remain under review. In this paper, we report a pediatric case of aHUS with anti-complement factor H autoantibodies, who was treated successfully with eculizumab.
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등록된 정보가 없습니다.
참고문헌 (13)
참고문헌 신청
Calvaruso L / 2019 / Deterioration in Clinical Status Is Not Enough to Suspend Eculizumab : A Genetic Complement-Mediated Atypical Hemolytic Uremic Syndrome Case Report / Case Rep Nephrol 2019:9264824
Brocklebank V / 2018 / Thrombotic Microangiopathy and the Kidney / Clin J Am Soc Nephrol 13:300~317
Fakhouri F / 2018 / Anticomplement Treatment in Atypical and Typical Hemolytic Uremic Syndrome / Semin Hematol 55:150~158
Dedhia P / 2017 / Eculizumab and Belatacept for De Novo Atypical Hemolytic Uremic Syndrome Associated With CFHR3-CFHR1Deletion in a Kidney Transplant Recipient : A Case Report / Transplant Proc 49:188~192
Farias JS / 2016 / A case of renal recovery in atypical hemolytic uremic syndrome treated with eculizumab / J Bras Nefrol 38:137~141
Brocklebank V / 2018 / Thrombotic Microangiopathy and the Kidney / Clin J Am Soc Nephrol 13:300~317
Fakhouri F / 2018 / Anticomplement Treatment in Atypical and Typical Hemolytic Uremic Syndrome / Semin Hematol 55:150~158
Dedhia P / 2017 / Eculizumab and Belatacept for De Novo Atypical Hemolytic Uremic Syndrome Associated With CFHR3-CFHR1Deletion in a Kidney Transplant Recipient : A Case Report / Transplant Proc 49:188~192
Farias JS / 2016 / A case of renal recovery in atypical hemolytic uremic syndrome treated with eculizumab / J Bras Nefrol 38:137~141
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