지원사업
학술연구/단체지원/교육 등 연구자 활동을 지속하도록 DBpia가 지원하고 있어요.
커뮤니티
연구자들이 자신의 연구와 전문성을 널리 알리고, 새로운 협력의 기회를 만들 수 있는 네트워킹 공간이에요.
논문 기본 정보
- 자료유형
- 학술저널
- 저자정보
- 발행연도
- 2017.1
- 수록면
- 165 - 168 (4page)
이용수
초록· 키워드
오류제보하기
Focal segmental glomerulosclerosis (FSGS) in children, which is a kind of nephrotic syndrome showing steroid resistance, usually progresses to a substantial number of end stage renal disease (ESRD). Although the pathogenesis of primary FSGS is unclear, several recent studies have reported that FSGS is associated with circulating immune factors such as soluble urokinase-type plasminogen activator receptor (suPAR) or anti-CD40 autoantibody. We report a successfully treated case of a 19-year-old female patient who experienced a recurrence of primary FSGS.
After the diagnosis of FSGS, the patient progressed to ESRD and received a kidney transplantation (KT). Three days later, recurrence was suspected through proteinuria and hypoalbuminemia. She has been performed plasmapheresis and high dose methylprednisolone pulse therapy and shown remission status without increasing proteinuria for four years after KT. In conclusion, strong immunosuppressive therapy may be helpful for a good prognosis of recurrent FSGS, suppressing several immunologic circulating factors related disease pathogenesis.
목차
등록된 정보가 없습니다.
참고문헌 (19)
참고문헌 신청
Assmann KJ / 2002 / Antibody-induced albuminuria and accelerated focal glomerulosclerosis in the Thy-1.1 transgenic mouse / Kidney Int 62 : 116 ~ 126
Baum MA / 2004 / Outcomes after renal transplantation for FSGS in children / Pediatr Transplant 8 : 329 ~ 333
Cochat P / 1996 / Management of recurrent nephrotic syndrome after kidney transplantation in children / Clin Nephrol 46 : 17 ~ 20
Cochat P / 2009 / Disease recurrence in paediatric renal transplantation / Pediatr Nephrol 24 : 2097 ~ 2108
D'Agati VD / 2011 / Focal segmental glomerulosclerosis / N Engl J Med 365 : 2398 ~ 2411
Baum MA / 2004 / Outcomes after renal transplantation for FSGS in children / Pediatr Transplant 8 : 329 ~ 333
Cochat P / 1996 / Management of recurrent nephrotic syndrome after kidney transplantation in children / Clin Nephrol 46 : 17 ~ 20
Cochat P / 2009 / Disease recurrence in paediatric renal transplantation / Pediatr Nephrol 24 : 2097 ~ 2108
D'Agati VD / 2011 / Focal segmental glomerulosclerosis / N Engl J Med 365 : 2398 ~ 2411
함께 읽어보면 좋을 논문
논문 유사도에 따라 DBpia 가 추천하는 논문입니다. 함께 보면 좋을 연관 논문을 확인해보세요!
-
Pathogenesis of Focal Segmental Glomerulosclerosis
Journal of Pathology and Translational Medicine
2016 .01
-
Circulating Permeability Factors in Idiopathic Nephrotic Syndrome
Childhood Kidney Diseases
2019 .01
-
Aberrant Blood Vessel Formation Connecting the Glomerular Capillary Tuft and the Interstitium Is a Characteristic Feature of Focal Segmental Glomerulosclerosis-like IgA Nephropathy
Journal of Pathology and Translational Medicine
2016 .01
-
A Case of Progressive FSGS and Chronic Kidney Disease in Congenital Chloride Diarrhea with SLC26A3 Mutation
대한유전성대사질환학회지
2018 .01
-
Experience with Pediatric Kidney Transplantation, 1985-2016: A Single Regional Center Study
Childhood Kidney Diseases
2017 .01
-
A Case of Secondary FSGS due to Chronic Chloride Diarrhea
Childhood Kidney Diseases
2016 .01
-
터너증후군 환자에서 발생한 국소분절사구체경화증 1예
고신대학교 의과대학 학술지
2015 .01
-
Dendritic Cell Dysfunction in Patients with End-stage Renal Disease
Immune Network
2017 .06
-
Trends in epidemiologic characteristics of end-stage renal disease from 2019 Korean Renal Data System (KORDS)
Kidney Research and Clinical Practice
2021 .01
-
The Impact of Obesity on Kidney Disease: Observational Cohort Study Analyzing 14,492 Kidney Biopsy Cases
Journal of Korean Medical Science
2024 .01
-
Gorham-Stout Syndrome with Focal Segmental Glomerulosclerosis: A Case Report
Childhood Kidney Diseases
2020 .01
-
Alterations in Structural and Functional Connectivities in Patients with End-Stage Renal Disease
Journal of Clinical Neurology
2020 .01
-
Bleeding after Endoscopic Resection in Patients with End-Stage Renal Disease on Dialysis: A Multicenter Propensity Score-Matched Analysis
Clinical Endoscopy
2020 .01
-
Clinical Characteristics and Long-Term Prognosis of Alport Syndrome: A Retrospective Single-Center Study
Childhood Kidney Diseases
2020 .01
-
Sugammadex administration in patients with end-stage renal disease: a narrative review with recommendations
Anesthesia and Pain Medicine
2023 .01
-
Clinical Features and Long-Term outcomes of Patients with Late Steroid Resistant/Sensitive Nephrotic Syndrome: A Single Center Study
Childhood Kidney Diseases
2015 .01
-
Effects of residential greenness on clinical outcomes of patients with chronic kidney disease: a large-scale observation study
Kidney Research and Clinical Practice
2021 .01
-
Malignancy after Pediatric Kidney Transplantation: The 30-Year Experience of a Single Center
Childhood Kidney Diseases
2020 .01
이 논문의 저자 정보
최근 본 자료
댓글(0)
0