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학술연구/단체지원/교육 등 연구자 활동을 지속하도록 DBpia가 지원하고 있어요.
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연구자들이 자신의 연구와 전문성을 널리 알리고, 새로운 협력의 기회를 만들 수 있는 네트워킹 공간이에요.
논문 기본 정보
- 자료유형
- 학술저널
- 저자정보
- 발행연도
- 2015.1
- 수록면
- 111 - 117 (7page)
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초록· 키워드
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Polyglandular autoimmune syndrome (PAS) is a group of syndromes comprised of glandular and extra-glandular disorders characterized by autoimmunity. A 57-year-old woman presented with acute progressive dyspnea and generalized weakness for several months. The patient was assessed to have acute congestive heart failure with cardiomyopathy, chronic renal failure with hyporeninemic hypoaldosteronism, and pancytopenia in addition to primary hypothyroidism and adrenal insufficiency. With the diagnosis of PAS type 2 complicated by multiple organ failure (MOF), medium-dose prednisolone (30 mg/d) was introduced primarily to control the activity of autoimmunity, which triggered MOF over the adrenal insufficiency. Levothyroxine (25 μg/d) was followed for replacement of the thyroid hormone deficiency. However, the symptoms and signs fluctuated, depending on the dosage of prednisolone, and progressively worsened by empty sella syndrome and aplastic anemia. Here, we report on a case of PAS type 2 with MOF and atypical complications, and suggest that recognition, assessment, and control of PAS as a systemic autoimmune disease may be essential.
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참고문헌 (12)
참고문헌 신청
Michels AW. / 2010 / Autoimmune polyglandular syndromes / Nat Rev Endocrinol 6:270~277
Neufeld M / 1980 / Autoimmune aspects of endocrine disorders / Academic Press :357~365
Betterle C. / 2003 / Update on autoimmune polyendocrine syndromes(APS) / Acta Biomed 74:9~33
Betterle C. / 2004 / Autoimmune polyglandular syndrome Type 2 : the tip of an iceberg? / Clin Exp Immunol 137:225~233
Chen QY / 2001 / Endocrinology. 4th ed / W.B. Saunders :587~599
Neufeld M / 1980 / Autoimmune aspects of endocrine disorders / Academic Press :357~365
Betterle C. / 2003 / Update on autoimmune polyendocrine syndromes(APS) / Acta Biomed 74:9~33
Betterle C. / 2004 / Autoimmune polyglandular syndrome Type 2 : the tip of an iceberg? / Clin Exp Immunol 137:225~233
Chen QY / 2001 / Endocrinology. 4th ed / W.B. Saunders :587~599
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