지원사업
학술연구/단체지원/교육 등 연구자 활동을 지속하도록 DBpia가 지원하고 있어요.
커뮤니티
연구자들이 자신의 연구와 전문성을 널리 알리고, 새로운 협력의 기회를 만들 수 있는 네트워킹 공간이에요.
논문 기본 정보
- 자료유형
- 학술저널
- 저자정보
- 발행연도
- 2019.1
- 수록면
- 26 - 30 (5page)
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초록· 키워드
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Hemophagocytic lymphohistiocytosis (HLH) is a hyperinflammatory syndrome caused by excessive activation of lymphocytes and macrophages, leading to cytokine storm. Infection-associated HLH is most common, and Epstein-Barr virus is the leading triggers. Quick diagnosis is essential for starting the treatment before irreversible damage. We report a case of 16-year-old boy who presented with unremitted fever, jaundice, and erythematous maculopapular rash all over the body. Investigations showed thrombocytopenia, hyperferritinemia, hypertriglycemia, and the bone marrow biopsy showed hemophagocytosis. Epstein-Barr virus antibody was positive. He responded to chemotherapy as per the HLH-2004 protocol and supportive treatment, and was discharged without complication on day 17.
목차
등록된 정보가 없습니다.
참고문헌 (18)
참고문헌 신청
Janka GE / 2014 / Hemophagocytic syndromes: an update / Blood Rev 28:135~142
Asano T / 2012 / Hemophagocytic lymphohistiocytosis after hematopoietic stem cell transplantation in children: a nationwide survey in Japan / Pediatr Blood Cancer 59:110~114
Okabe T / 2012 / What intensivists need to know about hemophagocytic syndrome: an underrecognized cause of death in adult intensive care units / J Intensive Care Med 27:58~64
Imashuku S / 2003 / Treatment of Epstein-Barr virus-associated hemophagocytic lymphohistiocytosis (EBV-HLH) in young adults: a report from the HLH study center / Med Pediatr Oncol 41:103~109
Chandrakasan S / 2013 / Hemophagocytic lymphohistiocytosis: advances in pathophysiology, diagnosis, and treatment / J Pediatr 163:1253~1259
Asano T / 2012 / Hemophagocytic lymphohistiocytosis after hematopoietic stem cell transplantation in children: a nationwide survey in Japan / Pediatr Blood Cancer 59:110~114
Okabe T / 2012 / What intensivists need to know about hemophagocytic syndrome: an underrecognized cause of death in adult intensive care units / J Intensive Care Med 27:58~64
Imashuku S / 2003 / Treatment of Epstein-Barr virus-associated hemophagocytic lymphohistiocytosis (EBV-HLH) in young adults: a report from the HLH study center / Med Pediatr Oncol 41:103~109
Chandrakasan S / 2013 / Hemophagocytic lymphohistiocytosis: advances in pathophysiology, diagnosis, and treatment / J Pediatr 163:1253~1259
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