지원사업
학술연구/단체지원/교육 등 연구자 활동을 지속하도록 DBpia가 지원하고 있어요.
커뮤니티
연구자들이 자신의 연구와 전문성을 널리 알리고, 새로운 협력의 기회를 만들 수 있는 네트워킹 공간이에요.
논문 기본 정보
- 자료유형
- 학술저널
- 저자정보
- 발행연도
- 2018.1
- 수록면
- 66 - 71 (6page)
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초록· 키워드
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A 15-year-old girl with Wilson’s disease complained of progressive proximal muscle weakness and difficulty with mastication aggravated by prolonged chewing with a diurnal variation for 3 weeks. Repetitive nerve stimulation using supramaximal stimuli revealed post-synaptic disorder and the needle electromyographic study showed the myopathic motor unit action potentials without any abnormal spontaneous activity in all sampled upper and lower limb muscles and the masseter, consistent with the suspicion of penicillamine-induced myasthenia gravis (PMG). The patient showed clinical improvement after discontinuation of D-penicillamine. Because of its favorable prognosis and curable treatment option, when proximal weakness with diurnal variation occurs after long-term administration of D-penicillamine, PMG should be suspected. In the electromyography laboratory, PMG should be distinguished from myositis and other neuromuscular diseases by performing the repetitive nerve stimulation test of proximal muscle recording. The discontinuation of penicillamine and administration of anticholinesterase are promptly considered to lead to better outcomes in those populations.
목차
등록된 정보가 없습니다.
참고문헌 (10)
참고문헌 신청
Roberts EA / 2008 / Diagnosis and treatment of Wilson disease: an update / Hepatology 47:2089~2111
Russell A / 1978 / Penicillamine induced myasthenia gravis associated with antibodies to acetylcholine receptor / Neurology 28:847~849
Jaffe IA / 1981 / Induction of auto-immune syndromes by penicillamine therapy in rheumatoid arthritis and other diseases / Semin Immunopathol 4:193~207
Andonopoulos A / 1994 / D-penicillamine induced myasthenia gravis in rheumatoid arthritis: An unpredictable common occurrence? / Clin Rheumatol 13:586~588
Fawcett PR / 1982 / D-penicillamine-associated myasthenia gravis: Immunological and electrophysiological studies / Muscle Nerve 5:328~334
Russell A / 1978 / Penicillamine induced myasthenia gravis associated with antibodies to acetylcholine receptor / Neurology 28:847~849
Jaffe IA / 1981 / Induction of auto-immune syndromes by penicillamine therapy in rheumatoid arthritis and other diseases / Semin Immunopathol 4:193~207
Andonopoulos A / 1994 / D-penicillamine induced myasthenia gravis in rheumatoid arthritis: An unpredictable common occurrence? / Clin Rheumatol 13:586~588
Fawcett PR / 1982 / D-penicillamine-associated myasthenia gravis: Immunological and electrophysiological studies / Muscle Nerve 5:328~334
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