지원사업
학술연구/단체지원/교육 등 연구자 활동을 지속하도록 DBpia가 지원하고 있어요.
커뮤니티
연구자들이 자신의 연구와 전문성을 널리 알리고, 새로운 협력의 기회를 만들 수 있는 네트워킹 공간이에요.
논문 기본 정보
- 자료유형
- 학술저널
- 저자정보
- 저널정보
- Asia Association for Disability and Oral Health International Journal of Disability and Oral Health International Journal of Disability and Oral Health Volume 18 Number 2
- 발행연도
- 2022.12
- 수록면
- 69 - 75 (7page)
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초록· 키워드
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Mitochondrial encephalomyopathy with lactic acidosis and stroke-like episodes (MELAS) syndrome is a rare disease caused by a mitochondrial DNA mutation. Patients with MELAS syndrome have physical restrictions that increase their risk of developing dental caries, and it can be challenging for them to receive dental care due to the possibility of seizures, vomiting, and mouthopening limitation. This report details the dental procedure performed on a 13-year-old girl with MELAS syndrome who had generalized mild hypomineralization of her permanent teeth. Dental caries on the occlusal surfaces of the mandibular second molars and maxillary first molars were restored with composite resin under general anesthesia. Patients with MELAS syndrome may benefit from dental treatment under careful general anesthesia. It is recommended to perform the procedure early in the morning and use the fluid containing 5% dextrose in place of lactate to reduce metabolic stress and prevent the progression of lactic acidosis. Some patients with MELAS syndrome may exhibit increased sensitivity to neuromuscular blockade, and sugammadex may be useful to counteract rocuronium’s effects. Additional flumazenil may help patients who regularly take benzodiazepines as antiepileptic medications recover from general anesthesia.
목차
Introduction
Case report
Discussion
Summary
References
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UCI(KEPA) : I410-ECN-0101-2023-515-000294048