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학술연구/단체지원/교육 등 연구자 활동을 지속하도록 DBpia가 지원하고 있어요.
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연구자들이 자신의 연구와 전문성을 널리 알리고, 새로운 협력의 기회를 만들 수 있는 네트워킹 공간이에요.
논문 기본 정보
- 자료유형
- 학술저널
- 저자정보
- 발행연도
- 2020.1
- 수록면
- 203 - 208 (6page)
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초록· 키워드
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Microscopic polyangiitis (MPA) is a small vessel vasculitides mostly associated with anti-neutrophil cytoplasmic antibodies (ANCA). The kidney is the most commonly affected organ in MPA. We report the case of a 9-year-old girl with ANCA-negative MPA who initially presented with respiratory symptoms, including cough, sputum, and dyspnea. Based on her symptoms, atypical pneumonia was suspected. Also, childhood interstitial lung disease was considered based on findings seen on chest CT. Despite initial improvement of symptoms with oral corticosteroid therapy, dyspnea with initiation of corticosteroid tapering was noted. A final diagnosis of MPA was made after lung biopsy. ANCA was negative in both the initial and repeat blood tests. Oral cyclophosphamide and prednisolone treatments led to full remission. Since then, the patient has been treated with low dose prednisolone and azathioprine for maintenance. A good treatment response was achieved and her clinical symptoms, pulmonary functions, and radiologic findings have since improved. Thus, early and precise diagnosis of MPA is crucial for remission induction and prevention of symptom relapse.
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참고문헌 (15)
참고문헌 신청
Jennette JC / 2013 / 2012 revised International Chapel Hill Consensus Conference nomenclature of vasculitides / Arthritis Rheum 65:1~11
Chung SA / 2010 / Microscopic polyangiitis / Rheum Dis Clin North Am 36:545~558
Calatroni M / 2017 / ANCA-associated vasculitis in childhood : recent advances / Ital J Pediatr 43:46
Iudici M / 2016 / Childhood-onset granulomatosis with polyangiitis and microscopic polyangiitis : systematic review and meta-analysis / Orphanet J Rare Dis 11:141
Cabral DA / 2016 / Comparing presenting clinical features in 48 children with microscopic polyangiitis to 183children who have granulomatosis with polyangiitis(Wegener’s) : an ARChiVe cohort study / Arthritis Rheumatol 68:2514~2526
Chung SA / 2010 / Microscopic polyangiitis / Rheum Dis Clin North Am 36:545~558
Calatroni M / 2017 / ANCA-associated vasculitis in childhood : recent advances / Ital J Pediatr 43:46
Iudici M / 2016 / Childhood-onset granulomatosis with polyangiitis and microscopic polyangiitis : systematic review and meta-analysis / Orphanet J Rare Dis 11:141
Cabral DA / 2016 / Comparing presenting clinical features in 48 children with microscopic polyangiitis to 183children who have granulomatosis with polyangiitis(Wegener’s) : an ARChiVe cohort study / Arthritis Rheumatol 68:2514~2526
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