지원사업
학술연구/단체지원/교육 등 연구자 활동을 지속하도록 DBpia가 지원하고 있어요.
커뮤니티
연구자들이 자신의 연구와 전문성을 널리 알리고, 새로운 협력의 기회를 만들 수 있는 네트워킹 공간이에요.
초록· 키워드
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Immunoglobulin G4-related sclerosing cholangitis (IgG4-SC) is a rare disease characterized by increased serum levels of IgG4and dense infiltration of IgG4-positive plasma cells with fibrosis in the bile duct wall. IgG4-SC is frequently associated withautoimmune pancreatitis (AIP) and typically shows an excellent response to steroid therapy. Despite recent progress inunderstanding the clinical presentation of IgG4-SC, its diagnosis still remains a challenge, particularly if it manifests as an isolatedhilar stricture with normal serum IgG4 concentrations. In this article, we report the case of a 75-year-old man with IgG4-SC inwhom it was difficult to distinguish hilar cholangiocarcinoma due to the normal serum IgG4 concentration and no accompanyingAIP. He had an indolent clinical course and showed slow progression of a bile duct lesion over 6 years.
목차
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참고문헌 (10)
참고문헌 신청
Ghazale A / 2008 / Immunoglobulin G4-associated cholangitis: clinical profile and response to therapy / Gastroenterology 134 : 706 ~ 715
Kamisawa T / 2003 / A new clinicopathological entity of IgG4?related autoimmune disease / J Gastroenterol 38 : 982 ~ 984
Kimura Y / 2012 / Pathologic significance of immunoglobulin G4-positive plasma cells in extrahepatic cholangiocarcinoma / Hum Pathol 43 : 2149 ~ 2156
Naitoh I / 2009 / Endoscopic transpapillary intraductal ultrasonography and biopsy in the diagnosis of IgG4-related sclerosing cholangitis / J Gastroenterol 44 : 1147 ~ 1155
Nakazawa T / 2010 / A case of advancedstage sclerosing cholangitis with autoimmune pancreatitis not responsive to steroid therapy / JOP 11 : 58 ~ 60
Kamisawa T / 2003 / A new clinicopathological entity of IgG4?related autoimmune disease / J Gastroenterol 38 : 982 ~ 984
Kimura Y / 2012 / Pathologic significance of immunoglobulin G4-positive plasma cells in extrahepatic cholangiocarcinoma / Hum Pathol 43 : 2149 ~ 2156
Naitoh I / 2009 / Endoscopic transpapillary intraductal ultrasonography and biopsy in the diagnosis of IgG4-related sclerosing cholangitis / J Gastroenterol 44 : 1147 ~ 1155
Nakazawa T / 2010 / A case of advancedstage sclerosing cholangitis with autoimmune pancreatitis not responsive to steroid therapy / JOP 11 : 58 ~ 60
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