지원사업
학술연구/단체지원/교육 등 연구자 활동을 지속하도록 DBpia가 지원하고 있어요.
커뮤니티
연구자들이 자신의 연구와 전문성을 널리 알리고, 새로운 협력의 기회를 만들 수 있는 네트워킹 공간이에요.
초록· 키워드
오류제보하기
Pulmonary alveolar proteinosis (PAP) is a rare disease characterized by the accumulation of lipoproteinaceous material in the distal air spaces. Secondary forms of PAP are caused by underlying diseases, in particular tumorous conditions, the most common of which are hematologic malignancies, such as chronic myeloid leukemia and myelodysplastic syndrome (MDS). We herein describe a case of atypical manifestation of PAP caused by MDS, which initially mimicked military tuberculosis with severe thrombocytopenia because of radiologic features showing necrotic mediastinal lymphadenopathies and diffuse bronchiolitis. A 46-year-old male visited the hospital complaining of coughing and general weakness and was presumptively diagnosed with military tuberculosis combined with MDS. He was treated with antituberculous medication, but the lung lesions did not improve and dyspnea only progressed. Finally, he underwent lung biopsy and was diagnosed with atypical pattern of PAP associated with MDS.
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참고문헌 (8)
참고문헌 신청
Cordonnier C / 1994 / Secondary alveolar proteinosis is a reversible cause of respiratory failure in leukemic patients / Am J Respir Crit Care Med 149 (3 Pt 1) : 788 ~ 794
Park E / 2012 / Pulmonary alveolar proteinosis as an unusual pattern of lung involvement in Sjogren syndrome / Rheumatol Int 32 : 2945 ~ 2948
Seymour JF / 2002 / Pulmonary alveolar proteinosis: progress in the first 44 years / Am J Respir Crit Care Med 166 : 215 ~ 235
Tabata S / 2009 / Successful allogeneic bone marrow transplantation for myelodysplastic syndrome complicated by severe pulmonary alveolar proteinosis / Int J Hematol 90 : 407
Trapnell BC / 2003 / Pulmonary alveolar proteinosis / N Engl J Med 349 : 2527 ~ 2539
Park E / 2012 / Pulmonary alveolar proteinosis as an unusual pattern of lung involvement in Sjogren syndrome / Rheumatol Int 32 : 2945 ~ 2948
Seymour JF / 2002 / Pulmonary alveolar proteinosis: progress in the first 44 years / Am J Respir Crit Care Med 166 : 215 ~ 235
Tabata S / 2009 / Successful allogeneic bone marrow transplantation for myelodysplastic syndrome complicated by severe pulmonary alveolar proteinosis / Int J Hematol 90 : 407
Trapnell BC / 2003 / Pulmonary alveolar proteinosis / N Engl J Med 349 : 2527 ~ 2539
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