지원사업
학술연구/단체지원/교육 등 연구자 활동을 지속하도록 DBpia가 지원하고 있어요.
커뮤니티
연구자들이 자신의 연구와 전문성을 널리 알리고, 새로운 협력의 기회를 만들 수 있는 네트워킹 공간이에요.
논문 기본 정보
- 자료유형
- 학술저널
- 저자정보
- 발행연도
- 2013.1
- 수록면
- 204 - 209 (6page)
이용수
초록· 키워드
오류제보하기
Eisenmenger syndrome is a severe form of pulmonary arterial hypertension related to congenital cardiac defects. Many patients die at a young age from such complications. The treatment of primary pulmonary hypertension is being applied to Eisenmenger syndrome such as endothelin receptor antagonists, phosphodiesterase-5 blockers, and prostacyclin. We experienced a case of 29-year female with ventricular septal defect-related Eisenmenger syndrome complicated with Down syndrome and Moyamoya disease, who was admitted to intensive care unit due to enteritis-associated septic shock. After the combination treatment with iloprost and sildenafil within the intensive care unit, the patient was able to wean mechanical ventilation without further applications of invasive rescue therapy such as extracorporeal membrane oxygenator. She was later discharged with bosentan. She maintained bosentan therapy for 34 months continuously without aggravations of symptom but eventually died with intracranial hemorrhage, a complication of Moyamoya disease. To our knowledge, this is the first case report of Eisenmenger syndrome accompanied by mosaic Down syndrome and Moyamoya disease.
목차
등록된 정보가 없습니다.
참고문헌 (20)
참고문헌 신청
Kainth DS / 2013 / Prevalence and characteristics of concurrent down syndrome in patients with moyamoya disease / Neurosurgery 72:210~215
Albertini M / 2001 / Improvement of respiratory function by bosentan during endotoxic shock in the pig / Prostaglandins Leukot Essent Fatty Acids 65 : 103 ~ 108
Avila-Alvarez A / 2012 / Inhaled iloprost as a rescue therapy for transposition of the great arteries with persistent pulmonary hypertension of the newborn / Pediatr Cardiol
Belohlavek J / 2010 / Veno-arterial ECMO in severe acute right ventricular failure with pulmonary obstructive hemodynamic pattern / J Invasive Cardiol 22 : 365 ~ 369
Daliento L / 1998 / Eisenmenger syndrome. Factors relating to deterioration and death / Eur Heart J 19 : 1845 ~ 1855
Albertini M / 2001 / Improvement of respiratory function by bosentan during endotoxic shock in the pig / Prostaglandins Leukot Essent Fatty Acids 65 : 103 ~ 108
Avila-Alvarez A / 2012 / Inhaled iloprost as a rescue therapy for transposition of the great arteries with persistent pulmonary hypertension of the newborn / Pediatr Cardiol
Belohlavek J / 2010 / Veno-arterial ECMO in severe acute right ventricular failure with pulmonary obstructive hemodynamic pattern / J Invasive Cardiol 22 : 365 ~ 369
Daliento L / 1998 / Eisenmenger syndrome. Factors relating to deterioration and death / Eur Heart J 19 : 1845 ~ 1855
이 논문의 저자 정보
최근 본 자료
댓글(0)
0